A 9-month-old male is evaluated for lactic acidosis and increased levels of serum alanine. He is diagnosed with pyruvate dehydrogenase complex deficiency and placed on a special diet by the physician.

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Principles of Therapeutics

Question

A 9-month-old male is evaluated for lactic acidosis and increased levels of serum alanine. He is diagnosed with pyruvate dehydrogenase complex deficiency and placed on a special diet by the physician. This special diet most likely consists of

Options

Aalanine
Basparagine
Chistidine
Dleucine
Eserine

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Topics

#pyruvate dehydrogenase deficiency#ketogenic diet#leucine#lactic acidosis

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